HIRSCHSPRUNG’S DISEASE IN CHILDREN
DOI:
https://doi.org/10.61699/cjmps-v1-i4-p38-43Keywords:
Hirschsprung’s disease, Megacolon, Congenital megacolon, Toxic megacolonAbstract
Hirschsprung’s disease – megacolon - is a congenital anomaly, characterized by theabsence of nerve cells - ganglia in certain segments of the intestine, which is accompaniedby complete or partial functional obstruction of the intestines.Among the clinical complaints, it is worth noting: weight loss, it is possible to developanorexia, various types of physical development disorders, chronic constipation, flatulence,big belly and defecation disorders cause nervous system dysfunction.Early diagnosis is important, the longer the diagnosis is delayed, the greater the damagesymptoms and the risk of developing toxic processes - toxic megacolon, whichsometimes ends with fatal results.The aim of our work today is to diagnose 3-year-old and 15-year-old patients with similarclinical complaints.On the X-rays, the expansion of the rectum and sigmoid colon was observed, the mucousmembrane is rough, the sigmoid colon is long, the intestines remain dilated afterdefecation, a significant part of the contrast agent is in the intestines, the functionalcondition of the intestines is impaired - congenital megacolon - Hirschsprung’s disease.
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